Tracheobronchomalacia (TBM) is a rare congenital disease. Early diagnosis of TBM plays an indispensable role. Aim: Early detection of the primary patient with severe tracheobronchomalacia helps in performing suficient surgical treatment. Methods. Child born on 05.05.2019, detected with tracheobronhomalacia in the first month of life. Oxigen dependent child shows up to 60% desaturation on free breathing. Child hospitalized in the Department of reanimation and intensive therapy with TBM in May 2019 – to present. The diagnosis was confirmed by instrumental examination: chest x-ray, pulmonary CT, bronchoscopy. Results: Oxigen dependent child from the birth shows at chest x-ray bilaterally pneumonia and polyresistant germs (Pseudomonas aeruginosa; Stenotrophomonas maltophilia, Klebsiella pneumoniae; Staphylococcus aureus; Enterobacter aerogenes). CT pulmonary shows appearance of stricture of the trachea and bronchi. Bronchoscopy – the appearance of collapsed airways which is easily restored after inhalation of air. This child for more than 3 years is assisted with VAP through a tracheostomy. The growth and development of the child correspond to the age with some motor deficiencies in the lower limbs. Concusions: The child needs monitoring by a multidisciplinary team: interventional pneumologist, radiologists, thoracic surgeons, infectious disease doctors, geneticists, ENT, neurologists. Posibility of serious complications leading to death shows the importance of developing appropriate treatment tactics for the presented child.