Tumora Klatskin: diagnosticul, tratamentul si rezultatul la distanta (caz clinic)
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GUŢU, Eugen, IACUB, Vladimir, ABABII, Tudor, CUMPATA, Serghei. Tumora Klatskin: diagnosticul, tratamentul si rezultatul la distanta (caz clinic). In: Chirurgia (București, Romania), 2018, nr. S1(113), pp. 222-223. ISSN 1221-9118.
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Chirurgia (București, Romania)
Numărul S1(113) / 2018 / ISSN 1221-9118

Tumora Klatskin: diagnosticul, tratamentul si rezultatul la distanta (caz clinic)

Klatskin tumor: diagnostic, treatment and long-term outcome (clinical case)


Pag. 222-223

Guţu Eugen, Iacub Vladimir, Ababii Tudor, Cumpata Serghei
 
Universitatea de Stat de Medicină şi Farmacie „Nicolae Testemiţanu“
 
 
Disponibil în IBN: 14 decembrie 2021


Rezumat

Introducere: Colangiocarcinomul perihilar (tumora Klatskin) reprezinta o afectiune canceroasa a bifurcatiei arborelui biliar, ce se
manifesta prin aparitia timpurie a sindromului de icter mecanic. In pofida acestui fapt, majoritatea bolnavilor la momentul diagnosticarii
prezinta o forma local avansata a tumorii, cu invazia structurilor anatomice invecinate, fapt ce indica efectuarea operatiei
paliative, cu scop de solutionare doar a sindromului de icter mecanic. Pentru un tratament definitiv al bonavului cu tumora Klatskin
se impune ablatia tumorii cu refacerea continuitatii arborelui biliar. Supravietuirea bolnavilor cu tumora Klatskin dupa tratamentul
chirurgical radical este relativ mica, alcatuind o rata de 65% la un an postoperator, 58% la doi ani si 31,9% la cinci ani. Cazul
clinic: O pacienta de 47 ani cu un tablou clinic de icter mecanic. Diagnosticul de tumora Klatskin, Bismuth-Corlette IIIB este stabilit
in baza ecografiei, MRCP si a parametrilor biochimici sanguini. Operatia: Rezectia de colangiocarcinom hilar cu hepatectomie
partiala (segmente I, II, III, IV a ficatului), rezectie tangentiala de vena porta cu plastia ei, hepaticojejunostomie pe ansa Roux cu
drenarea cailor biliare tip Voelker. Evolutie postoperatorie favorabila cu externare la a 30-a zi postoperator. Cazul clinic prezentat
releva supravietuirea pacientei dupa o operatie radicala in caz de colangiocarcinom hilar mai mult de doi ani si sase luni pina in
momentul actual. Concluzii: diagnosticul de tumoare Klatskin se bazeaza pe examinarile ecografice, MRCP æi a rezultatelor analizelor
biochimice ale sangelui; singura optiune de prelungire a vietii bolnavului cu colangiocarcinom hilar este operatia radicala de
ablatie completa a tumorii cu refacerea continuitatii arborelui biliar.



Introduction: Perihilar cholangiocarcinoma (Klatskin tumor) is a malign tumor arising from the extrahepatic bile duct bifurcation,
which is manifested by early appearance of mechanical jaundice syndrome. Despite this, most patients at the time of diagnosis
present a locally advanced tumor with the invasion of neighbouring anatomical structures, that serves as an indication for palliative
surgery, solving just the syndrome of mechanical jaundice. For definitive treatment of patient with Klatskin tumor, the ablation of
tumour with bile duct reconstruction is required. The survival of the patients after definitive surgery for Klatskin tumor are relative
low: 65% after one year post surgery, 58% after two years and 31.9% after five years. Clinical case: Patient B., a 47-year-old women,
with presentation of mechanical jaundice. Diagnosis of Klatskin tumor, Bismuth-Corlette IIIB was confirmed by ultrasound, MRCP
and biochemistry analysis of blood. Performed surgery: Resection of hilar cholangiocarcinoma with partial hepat-ectomy (I, II, III,
IV liver segments), tangential resection of portal vein with its stitching and Roux-Y hepatico-jejunostomy with Voelker drainage of
bile duct. Favourable post-operative evolution with discharging from the hospital in 30 days after surgery. The presented case reveals
the survival of one patient after radical surgery for Klatskin tumor more than two years and six mounts to date. Conclusions: The
diagnosis of Klatskin tumor is based on the ultrasound, MRCP and biochemistry analysis of blood; the only option to extend the life
of the patient with hilar cholangiocarcinoma is the radical surgery - complete ablation of the tumor with restoration of biliary tree
continuity.



Cuvinte-cheie
tumora Klatskin, icter mecanic, tratament chirurgical, cholangiocarcinom,

Klatskin tumour, mechanical jaundice, surgical treatment, cholangiocarcinoma