Conţinutul numărului revistei |
Articolul precedent |
Articolul urmator |
987 14 |
Ultima descărcare din IBN: 2024-03-26 17:13 |
Căutarea după subiecte similare conform CZU |
616.23-007.61-008-053.2 (1) |
Заболевания дыхательной системы (757) |
SM ISO690:2012 ŞCIUCA, Svetlana, SELEVESTRU, Rodica, BURLAC-PASAT, Cristina, NALBUŞ, Olesea, BIVOL, Natalia, COTOMAN, Aliona. Afectarea sistemului respirator la diferite etape de vârstă în sindromul Marfan la copii.. In: Buletinul Academiei de Ştiinţe a Moldovei. Ştiinţe Medicale, 2016, nr. 1(50), pp. 119-123. ISSN 1857-0011. |
EXPORT metadate: Google Scholar Crossref CERIF DataCite Dublin Core |
Buletinul Academiei de Ştiinţe a Moldovei. Ştiinţe Medicale | ||||||
Numărul 1(50) / 2016 / ISSN 1857-0011 | ||||||
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CZU: 616.23-007.61-008-053.2 | ||||||
Pag. 119-123 | ||||||
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Descarcă PDF | ||||||
Rezumat | ||||||
În articol sunt prezentate cazuri de sindrom Marfan la diferite etape de vârstă: 9 luni și 8 ani, cu scop de a evidenția modifi cările pulmonare specifi ce. Diagnosticul clinic a fost stabilit în baza criteriilor Gent, care în 86% din cazuri pot confi rma sau exclude sindromul Marfan. Deși, afectarea pulmonară nu reprezintă o caracteristică de bază a patologiei date, la majoritatea pacienților se depistează modifi cări pulmonare histologice: chistice, emfi zematoase, fi broase, pneumonii sau bronșiectazii în focar. |
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Cuvinte-cheie sindromul Marfan, pulmoni, copil |
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Cerif XML Export
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Diagnosticul clinic a fost stabilit în baza criteriilor Gent, care în 86% din cazuri pot confi rma sau exclude sindromul Marfan. Deși, afectarea pulmonară nu reprezintă o caracteristică de bază a patologiei date, la majoritatea pacienților se depistează modifi cări pulmonare histologice: chistice, emfi zematoase, fi broase, pneumonii sau bronșiectazii în focar. </cfAbstr> <cfAbstr cfLangCode='EN' cfTrans='o'>Respiratory system damage in children of different ages with Marfan syndrome This article presents cases with Marfan syndrome in different child ages: 9 months and 8 years, for revealing the specifi c pulmonary modifi cations. The clinical diagnosis is made using the Ghent nosology, which defi nitely diagnose Marfan syndrome in 86% of cases. 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