Sindromul siringomielic în cadrul osteocondropatiei juvenile vertebrale scheuermann mau. (Prezentare de caz clinic)
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GHERMAN, Diomid, SANGHELI, Marina, PLEŞCA, Svetlana, VAŞCHEVICI, Rodica. Sindromul siringomielic în cadrul osteocondropatiei juvenile vertebrale scheuermann mau. (Prezentare de caz clinic) . In: Analele Ştiinţifice ale USMF „N. Testemiţanu”, 2010, nr. 3(11), pp. 475-479. ISSN 1857-1719.
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Analele Ştiinţifice ale USMF „N. Testemiţanu”
Numărul 3(11) / 2010 / ISSN 1857-1719

Sindromul siringomielic în cadrul osteocondropatiei juvenile vertebrale scheuermann mau. (Prezentare de caz clinic)

Pag. 475-479

Gherman Diomid1, Sangheli Marina1, Pleşca Svetlana2, Vaşchevici Rodica1
 
1 Universitatea de Stat de Medicină şi Farmacie „Nicolae Testemiţanu“,
2 Institutul de Neurologie si Neurochirurgie ”Diomid Gherman”
 
 
Disponibil în IBN: 16 decembrie 2013


Rezumat

Syringomielinic syndrome associated with vertebral juvenile osteochondropathy Scheuermann Mau It was described a clinical case of the patient V, aged 57 with vertebral juvenile osteochondropathy Scheuermann Mau associated with. At the age of 40 the patient develops sensitive disturbances at the lower level of cervical region and the upper level of thoracic region. Magnetic resonance of the cervical and thoracic level revealed asymmetric cavities at the Th1- Th7, thoracic kyphosis with cuneiform vertebras at the Th6-Th11 level, without signs of discoradicular and medullar contact. In conclusion it was suggested that vertebral juvenile osteochondropathy Scheuermann Mau associated with syringohydromielinic syndrome is determined by fibrotic process of meninx (fibrotic arachnoiditis) as a result of medular ischemia with intramedular cavities.

A fost descris un caz clinic al pacientului V. în vârstă de 57 de ani cu osteocondropatie vertebrală juvenilă Scheuermann-Mau şi sindrom siringomielic. La vârsta de 40 de ani la pacient survin tulburări de sensibilitate de la nivelul regiunilor cervicală inferioară şi toracală superioară. La IRM cervico-toracală la nivelul segmentelor Th1-Th7 au fost vizualizate cavităţi asimetrice, chifoză toracală cu vertebre cuneiforme Th6-Th11, fără semne de contact disco-radicular şi medular. În concluzie s-a sugerat că sindromul siringomielic în cadrul osteocondropatiei juvenile Scheuermann Mau a fost provocat de procesul fibrozant al meningelor (arahnoidita fibrozantă), care au dus la ischemia vaselor măduvei spinării şi respectiv la formarea cavităţilor medulare.

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