Cutaneous mesenchymal neoplasms are a heterogeneous group of relatively rare tumors, arising in the skin and characterized by clinicopathological heterogeneity. Benign mesenchymal tumors are more frequent than their malignant counterparts. Clinically important, dermal sarcomas of some lines of differentiation are associated with a favorable clinical prognosis, independent of the histological grading, which is important to know for the correct treatment of patients. The etiology is often unknown, sometimes there is an association with insults such as radiation, scars, or lymphedematous or venous stasis.