Spontaneous pneumothorax: congenital cystic adenomatoid malformation of the lung
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CUTITARI, Alina. Spontaneous pneumothorax: congenital cystic adenomatoid malformation of the lung. In: MedEsperaInternational Medical Congress for Students and Young Doctors. 7, 3-5 mai 2018, Chişinău. Chisinau, Republic of Moldova: 2018, pp. 37-38.
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MedEspera
7, 2018
Congresul "International Medical Congress for Students and Young Doctors"
7th edition, Chişinău, Moldova, 3-5 mai 2018

Spontaneous pneumothorax: congenital cystic adenomatoid malformation of the lung


Pag. 37-38

Cutitari Alina
 
”Nicolae Testemițanu” State University of Medicine and Pharmacy
 
Disponibil în IBN: 2 noiembrie 2020


Rezumat

Background. Congenital cystic adenomatoid malformation (CCAM) is a rare developmental abnormality of the lung with an incidence of 1 in 25,000 to 1 in 35,000 pregnancies and represents 25% of congenital lung malformations and 95% of congenital lung lesions, males and females being equally affected. It is characterized by multicystic mass arising in the lung parenchyma from abnormal proliferation of the immature terminal respiratory bronchioles. The clinical spectrum is wide and ranges from silent incidental lesions to severe congenital respiratory distress or stillbirths. The diagnosis of CCAM can be made in utero by prenatal ultrasongraphy and postnatally by imaging radiography and CT. We report a case of a CCAM, which provoked spontaneous pneumothorax. Case report. Ei ght month old patient was delivered to the Emergency Department at Institution of Mother and Child with pneumonia and left spontaneous pneumothorax. From the anamnesis, after birth was discovered CCAM after which the patient took a conservative treatment. On examination the patient was agitated, presented acrocyanosis, the general condition of the patient was severe. Chest X ray showed a large left sided pneumothorax with mediastinal shift to right and air containing cystic area of left lower lobe. Pneumoth orax was drained immediately, drain tube was seen through left 5th intercostal space. CT scan control of the chest showed expanded left lung with multiple cystic lesion in the lower lobe. After pre operative preparation lower left lobectomy was perfomed. A ccording classification by Stocker (1977), our patient had CCAM, tip I. Conclusions. Long term outcome is good in surgically managed asymptomatic patients with some studies showing only slight decrease in lung volume. Congenital cystic adenomatoid malforma tion of lung can cause severe respiratory distress but early diagnosis and surgical intervention can improve the condition and prevent death due to respiratory failure. The potential postnatal complications of CCAM include spontaneous pneumothorax, haemopn eumothorax and pyopneumothorax, increased likelihood of malignancies such as bronchoalveolar carcinoma.

Cuvinte-cheie
congenital cystic adenomatoid malformation, Diagnosis, pneumothorax